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:: Volume 25, Issue 2 (Iranian Journal of Ophthalmology 2013) ::
2013, 25(2): 167-170 Back to browse issues page
Spontaneous Scleral Perforation and Optic Nerve Dural Ectasia in Marfan Syndrome
Farideh Sharifipour Dr. * , Mahmoodreza Panahi-Bazaz Dr., Mohammad Malekahmadi Dr., Akbar Takhtaeian Dr.
, sharifipourf@yahoo.com
Abstract:   (7664 Views)

Purpose : To report two patients with spontaneous scleral perforation and bleb formation associated with Marfan syndrome (MFS) which one of them also showed bilateral optic nerve dural ectasia.

Case reports : An 11-year-old girl was referred with progressive myopia. Past medical history was negative. Slit-lamp examination revealed bilateral scleral thinning and perforation with bleb formation, shallow anterior chamber (AC), and microspherophakia. Systemic evaluation confirmed the diagnosis of MFS. B-scan ultrasonography and orbital MRI showed bilateral optic nerve dural ectasia. A 23-year-old man, known case of MFS, also presented with spontaneous scleral perforation with bleb formation and microspherophakia. In this case, ancillary tests didn't show optic nerve dural ectasia. Both patients underwent lensectomy with vitrectomy and iris-fixated intraocular lens implantation in both eyes.

Conclusion : MFS may be associated with new and rare findings as part of generalized connective tissue disorder.

   

Iranian Journal of Ophthalmology 201325(2):167-170 © 2013 by the Iranian Society of Ophthalmology

Keywords: Scleral Perforation, Optic Nerve, Dural Ectasia, Marfan Syndrome
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Type of Study: Case report | Subject: Anterior segment
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Sharifipour F, Panahi-Bazaz M, Malekahmadi M, Takhtaeian A. Spontaneous Scleral Perforation and Optic Nerve Dural Ectasia in Marfan Syndrome. Iranian Journal of Ophthalmology. 2013; 25 (2) :167-170
URL: http://irjo.org/article-1-826-en.html


Volume 25, Issue 2 (Iranian Journal of Ophthalmology 2013) Back to browse issues page
مجله چشم پزشکی ایران Iranian Journal of Ophthalmology
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